Association of Behçet’s Disease with Osteogenesis Imperfecta in A Ten-Year-Old Girl

Authors

  • M. Mehryar Department of Ophthalmology, Shiraz University of Medical Sciences, Shiraz
  • S.M. Hakim Department of Rheumatology, Shiraz University of Medical Sciences, Shiraz
  • Sh. Samangooei Department of Rheumatology, Shiraz University of Medical Sciences, Shiraz
Abstract:

Osteogenesis Imperfecta (OI) is a genetic disorder characterized by bones that break easily, often from little or no apparent cause. In this article, we present a patient suffering from OI, who had concomitant active Behçet’s Disease(BD)with repeated oro-genital ulcers, skin postular eruptions and severe recurrent bilateral uveitis. This patient, is, to our knowledge the first reported case in literature.

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Journal title

volume 26  issue 3-4

pages  171- 173

publication date 2001-12-01

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